An interesting case report on Herlyn-Werner-Wunderlich syndrome with hematoclopos and communicating blind duplex ureters

Abstract

Herlyn-Werner-Wunderlich syndrome represents a complex female genital malformation with uterus didelphys, unilateral low vaginal obstruction, and ipsilateral renal agenesis, all being secondary to mesonephric duct-induced müllerian anomalies. Clinically, this often presents in postpubertal adolescent or adult women where hematometrocolpos produces a more pronounced mass effect and pain on the side of the obstructed hemivagina. Mullerian duct anomalies have an incidence of 2-3%, while OBSTRUCTED HEMIVAGINA AND IPSILATERAL RENAL ANOMALY [OHVIRA] has an incidence of 0.1-3.5% of all such anomalies.[1,2] We hereby report a similar case which had in addition, duplication of the ipsilateral ureter with ectopic opening in the urethra and communication with hematocolpos making it even more rare.